Anesthesia and pain management of a patient with Kleefstra Syndrome for robotic ureteral reimplantation.
Kleefstra syndrome (KS) is a genetic disorder caused by a microdeletion in the 9q34.3 chromosome with related clinical conditions requiring surgical intervention and careful consideration for anesthetic management includ- ing potential difficult airway, cardiac and neurological considerations, pulmo...
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| Main Authors: | , , , |
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| Format: | Book |
| Published: |
Pediatric Anesthesia and Critical Care Journal,
2023-07-01T00:00:00Z.
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| Online Access: | Connect to this object online. |
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| Summary: | Kleefstra syndrome (KS) is a genetic disorder caused by a microdeletion in the 9q34.3 chromosome with related clinical conditions requiring surgical intervention and careful consideration for anesthetic management includ- ing potential difficult airway, cardiac and neurological considerations, pulmonary infections, reflux and delayed gastric emptying, genitourinary abnormalities, hypoto- nia, and seizure disorders. In addition, we observed unique perioperative pain control considerations. We pre- sent a clinical case involving a 2-year-old female who re- ceived anesthesia for robotic ureteral reimplantation sur- gery. Perioperative implications are discussed and con- siderations for anesthetic care provided. |
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| Item Description: | 10.14587/paccj.2023.12 2281-8421 |