Carcinoid Syndrome-Induced Scleroderma-Like Disease

Scleroderma is a rare complication of carcinoid syndrome and is usually encountered in the setting of a metastatic primary neuroendocrine tumour of the distal ileum. Associated endocardial fibrosis is a frequent finding and the condition carries a poor prognosis. We report a case of scleroderma occu...

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Bibliographic Details
Main Authors: Karen Koch (Author), Wayne Grayson (Author)
Format: Book
Published: MDPI AG, 2019-06-01T00:00:00Z.
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042 |a dc 
100 1 0 |a Karen Koch  |e author 
700 1 0 |a Wayne Grayson  |e author 
245 0 0 |a Carcinoid Syndrome-Induced Scleroderma-Like Disease 
260 |b MDPI AG,   |c 2019-06-01T00:00:00Z. 
500 |a 2296-3529 
500 |a 10.1159/000496388 
520 |a Scleroderma is a rare complication of carcinoid syndrome and is usually encountered in the setting of a metastatic primary neuroendocrine tumour of the distal ileum. Associated endocardial fibrosis is a frequent finding and the condition carries a poor prognosis. We report a case of scleroderma occurring in a 72-year-old female with metastatic neuroendocrine carcinoma and associated pericardial fibrosis. The use of an alternative nomenclature such as "scleroderma-like" or "sclerodermoid" disease is proposed in order to emphasise its distinction from true idiopathic scleroderma, despite the histopathological similarities on skin biopsy. 
546 |a EN 
690 |a Carcinoid syndrome 
690 |a Scleroderma 
690 |a Scleroderma-like disorders 
690 |a Sclerodermoid disease 
690 |a Skin 
690 |a Dermatology 
690 |a RL1-803 
655 7 |a article  |2 local 
786 0 |n Dermatopathology, Vol 6, Iss 2, Pp 99-104 (2019) 
787 0 |n https://www.karger.com/Article/FullText/496388 
787 0 |n https://doaj.org/toc/2296-3529 
856 4 1 |u https://doaj.org/article/0e4a7da5a527485c8ac79a5de37e901f  |z Connect to this object online.