Albright hereditary osteodystrophy: dental management case report

Albright hereditary osteodystrophy is a disorder comprising phenotypic characteristics of genetic origin, such as short stature, obesity, and brachydactyly. It is a rare disorder and is related to pseudohypoparathyroidism. Within dentistry, it may be associated with enamel hypoplasia and late erupti...

Full description

Saved in:
Bibliographic Details
Main Authors: Stephanie Anagnostopoulos FRIEDRICH (Author), Jonas RODRIGUES (Author), Berenice Barbachan e SILVA (Author)
Format: Book
Published: Faculdade São Leopoldo Mandic, 2018-03-01T00:00:00Z.
Subjects:
Online Access:Connect to this object online.
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Albright hereditary osteodystrophy is a disorder comprising phenotypic characteristics of genetic origin, such as short stature, obesity, and brachydactyly. It is a rare disorder and is related to pseudohypoparathyroidism. Within dentistry, it may be associated with enamel hypoplasia and late eruption. Furthermore, due to neurological problems, these patients may impose behavioural difficulties during dental appointments. The present study aims to describe the case of a patient with a possible diagnosis of Albright hereditary osteodystrophy, presenting symptoms and limitations to dental management.
Item Description:http://dx.doi.org/10.1590/1981-863720180001000153289
0103-6971
1981-8637