Bullous Mastocytosis Mimicking Congenital Epidermolysis Bullosa

A 2-month-old female infant was referred to DebRA Mexico from the Regional Children's Hospital because of a generalized dermatosis from birth characterized by multiple blisters and erosions on the trunk, face and limbs, associated with minor trauma. A skin biopsy showing subepidermal blisters a...

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Bibliographic Details
Main Authors: Julio Cesar Salas-Alanis (Author), Cesar Eduardo Rosales-Mendoza (Author), Jorge Ocampo-Candiani (Author)
Format: Book
Published: Karger Publishers, 2014-05-01T00:00:00Z.
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Summary:A 2-month-old female infant was referred to DebRA Mexico from the Regional Children's Hospital because of a generalized dermatosis from birth characterized by multiple blisters and erosions on the trunk, face and limbs, associated with minor trauma. A skin biopsy showing subepidermal blisters associated with a dermal infiltrate of Giemsa-positive cells and CD117-positive antibody was consistent with the diagnosis of bullous mastocytosis. Treatment with oral antihistamines, topical steroids, and antibiotics was initiated, leading to a remission of the lesions.
Item Description:1662-6567
10.1159/000362755