Excellent response to adalimumab in a patient with Papillon-Lefèvre syndrome: A case report
Abstract Papillon-Lefèvre syndrome (PLS) is a rare autosomal recessive disease that presents clinically with palmoplantar keratoderma and periodontitis and results in early‐onset dental loss. PLS management is difficult. We report a 30‐year‐old female with PLS who had unfavourable response to topica...
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| Main Authors: | , , , , |
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| Format: | Book |
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Wiley,
2023-09-01T00:00:00Z.
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| Summary: | Abstract Papillon-Lefèvre syndrome (PLS) is a rare autosomal recessive disease that presents clinically with palmoplantar keratoderma and periodontitis and results in early‐onset dental loss. PLS management is difficult. We report a 30‐year‐old female with PLS who had unfavourable response to topical keratolytic creams, oral isotretinoin and narrow‐band ultraviolet‐B (NB‐UVB) phototherapy but showed significant clinical improvement to adalimumab. |
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| Item Description: | 2768-6566 10.1002/jvc2.184 |