Multiple odontogenic keratocysts in Ehlers-Danlos syndrome: a rare case report

Abstract Background An odontogenic keratocyst is a lesion characterized by aggressive and infiltrative growth. The lesion is characterized by the existence of satellite microcysts (microtumours) and frequent recurrence (up to 30%). Ehlers-Danlos syndrome is a condition in which collagen production o...

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Main Authors: Anna Starzyńska (Author), Paulina Adamska (Author), Łukasz Adamski (Author), Aleksandra Sejda (Author), Piotr Wychowański (Author), Michał Studniarek (Author), Barbara Alicja Jereczek-Fossa (Author)
Format: Book
Published: BMC, 2021-03-01T00:00:00Z.
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Summary:Abstract Background An odontogenic keratocyst is a lesion characterized by aggressive and infiltrative growth. The lesion is characterized by the existence of satellite microcysts (microtumours) and frequent recurrence (up to 30%). Ehlers-Danlos syndrome is a condition in which collagen production or its post-translational modifications are affected. Defects in connective tissues cause symptoms, which range from mild joint hypermobility to life-threatening complications. Case presentation We present an extremely rare case of an 11-year old girl with Ehlers-Danlos syndrome and coexistence of multiple odontogenic keratocysts. Conclusions This case shows mainly atypical or rare association between multiple odontogenic keratocysts and Ehlers-Danlos syndrome.
Item Description:10.1186/s12903-021-01472-9
1472-6831