Multiple odontogenic keratocysts in Ehlers-Danlos syndrome: a rare case report
Abstract Background An odontogenic keratocyst is a lesion characterized by aggressive and infiltrative growth. The lesion is characterized by the existence of satellite microcysts (microtumours) and frequent recurrence (up to 30%). Ehlers-Danlos syndrome is a condition in which collagen production o...
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Main Authors: | , , , , , , |
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Format: | Book |
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BMC,
2021-03-01T00:00:00Z.
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Online Access: | Connect to this object online. |
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Summary: | Abstract Background An odontogenic keratocyst is a lesion characterized by aggressive and infiltrative growth. The lesion is characterized by the existence of satellite microcysts (microtumours) and frequent recurrence (up to 30%). Ehlers-Danlos syndrome is a condition in which collagen production or its post-translational modifications are affected. Defects in connective tissues cause symptoms, which range from mild joint hypermobility to life-threatening complications. Case presentation We present an extremely rare case of an 11-year old girl with Ehlers-Danlos syndrome and coexistence of multiple odontogenic keratocysts. Conclusions This case shows mainly atypical or rare association between multiple odontogenic keratocysts and Ehlers-Danlos syndrome. |
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Item Description: | 10.1186/s12903-021-01472-9 1472-6831 |