Rare association of hyper IgE syndrome with cervical rib and natal teeth
Hyper IgE syndrome (HIES) is a rare immunodeficiency syndrome characterized by a triad of cutaneous abscesses, mostly caused by <i>Staphylococus aureus</i>; pneumonia; and raised IgE levels. Nonimmunological associations include course facial features, multiple bone fractures, joint hype...
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| Main Authors: | , , , |
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| Format: | Book |
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Wolters Kluwer Medknow Publications,
2009-01-01T00:00:00Z.
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| Summary: | Hyper IgE syndrome (HIES) is a rare immunodeficiency syndrome characterized by a triad of cutaneous abscesses, mostly caused by <i>Staphylococus aureus</i>; pneumonia; and raised IgE levels. Nonimmunological associations include course facial features, multiple bone fractures, joint hyperextensibility, and retained primary dentition. Patients require long-term antibiotic therapy. We report here a classical case of HIES with rare associations of natal teeth, bilateral cervical ribs, and conductive deafness. The patient was being treated with monteleukast and dapsone. |
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| Item Description: | 0019-5154 1998-3611 |