Undifferentiated duodenal sarcoma with rhabdoid features
Tumors of the pediatric gastrointestinal tract are uncommon, with duodenal malignancies being extremely rare. Malignant rhabdoid tumor is a rare highly aggressive tumor that occurs in young children with a very poor clinical outcome. The tumor is characterized by a diffuse proliferation of "rha...
Saved in:
| Main Authors: | , |
|---|---|
| Format: | Book |
| Published: |
Elsevier,
2020-07-01T00:00:00Z.
|
| Subjects: | |
| Online Access: | Connect to this object online. |
| Tags: |
Add Tag
No Tags, Be the first to tag this record!
|
| Summary: | Tumors of the pediatric gastrointestinal tract are uncommon, with duodenal malignancies being extremely rare. Malignant rhabdoid tumor is a rare highly aggressive tumor that occurs in young children with a very poor clinical outcome. The tumor is characterized by a diffuse proliferation of "rhabdoid cells," which are round or polygonal with eccentric nuclei, prominent nucleoli, and glassy eosinophilic cytoplasm containing hyaline-like inclusion bodies. Very few cases of malignant tumors with rhabdoid features of the gastrointestinal tract are described in literature, but probably none so far in the duodenum of a pediatric patient. We present a case of a eleven year old with an undifferentiated tumour of the duodenum with rhabdoid features on histopathology, who underwent multimodality management and is doing well at 1 year of follow up. |
|---|---|
| Item Description: | 2213-5766 10.1016/j.epsc.2020.101451 |