Cystic biliary atresia masquerading as a choledochal cyst

Cystic biliary atresia is an uncommon form of biliary atresia that is often misdiagnosed as a choledochal cyst. Here we present a case of a neonate who presented with obstructive jaundice and an antenatally-detected abdominal cyst who was found to have cystic biliary atresia. The patient underwent a...

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Bibliographic Details
Main Authors: Carolyn Reuland (Author), Clint D. Cappiello (Author)
Format: Book
Published: Elsevier, 2021-11-01T00:00:00Z.
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Summary:Cystic biliary atresia is an uncommon form of biliary atresia that is often misdiagnosed as a choledochal cyst. Here we present a case of a neonate who presented with obstructive jaundice and an antenatally-detected abdominal cyst who was found to have cystic biliary atresia. The patient underwent a successful Kasai procedure for establishment of biliary flow. His initial post-operative course was complicated by three episodes of cholangitis requiring hospital admission. He is now two years out from Kasai portoenterostomy with normal bilirubin levels.
Item Description:2213-5766
10.1016/j.epsc.2021.102025