Familial "benign" pemphigus? Erythroderma and fatal outcome,

Abstract Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an un...

Full description

Saved in:
Bibliographic Details
Main Authors: Paula Baldissera Tansini (Author), Ana Letícia Boff (Author), Magda Blessmann Weber (Author), Renan Rangel Bonamigo (Author)
Format: Book
Published: Sociedade Brasileira de Dermatologia, 2020-03-01T00:00:00Z.
Subjects:
Online Access:Connect to this object online.
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Abstract Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome.
Item Description:0365-0596
10.1016/j.abd.2019.02.006