Idiopathic lymphoplasmacellular mucositis of the vulva in a patient with partial interferon-γ receptor 1 deficiency
We report a case of idiopathic lymphoplasmacellular mucositis (ILPM) of the vulva in a 48-year-old woman with partial interferon-γ receptor 1 (IFN-γR1) deficiency. The lesion had an unusual ulcerovegetative presentation. Remarkable response was observed with oral and topical steroids in the first 3...
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Wolters Kluwer Medknow Publications,
2019-01-01T00:00:00Z.
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| LEADER | 00000 am a22000003u 4500 | ||
|---|---|---|---|
| 001 | doaj_741540d23e2b4fef8cae6edfe91f6e13 | ||
| 042 | |a dc | ||
| 100 | 1 | 0 | |a Kuan-Yu Chen |e author |
| 700 | 1 | 0 | |a Tseng-Tong Kuo |e author |
| 700 | 1 | 0 | |a Ya-Ching Chang |e author |
| 700 | 1 | 0 | |a Rosaline Chung-Yee Hui |e author |
| 700 | 1 | 0 | |a Ya-Hui Chuang |e author |
| 245 | 0 | 0 | |a Idiopathic lymphoplasmacellular mucositis of the vulva in a patient with partial interferon-γ receptor 1 deficiency |
| 260 | |b Wolters Kluwer Medknow Publications, |c 2019-01-01T00:00:00Z. | ||
| 500 | |a 1027-8117 | ||
| 500 | |a 2223-330X | ||
| 500 | |a 10.4103/ds.ds_18_18 | ||
| 520 | |a We report a case of idiopathic lymphoplasmacellular mucositis (ILPM) of the vulva in a 48-year-old woman with partial interferon-γ receptor 1 (IFN-γR1) deficiency. The lesion had an unusual ulcerovegetative presentation. Remarkable response was observed with oral and topical steroids in the first 3 weeks. However, the lesion recurred after tapering oral steroids and continuous low-dose oral steroids were required to suppress recurrence. To the best of our knowledge, this is the first case report of ILPM in a patient with partial IFN-γR1 deficiency. ILPM should be included in the differential diagnosis of persistent vulvar ulcerovegetative lesions. | ||
| 546 | |a EN | ||
| 690 | |a Idiopathic lymphoplasmacellular mucositis | ||
| 690 | |a interferon-receptor 1 deficiency | ||
| 690 | |a vulva | ||
| 690 | |a Dermatology | ||
| 690 | |a RL1-803 | ||
| 655 | 7 | |a article |2 local | |
| 786 | 0 | |n Dermatologica Sinica, Vol 37, Iss 1, Pp 50-52 (2019) | |
| 787 | 0 | |n http://www.dermsinica.org/article.asp?issn=1027-8117;year=2019;volume=37;issue=1;spage=50;epage=52;aulast=Chen | |
| 787 | 0 | |n https://doaj.org/toc/1027-8117 | |
| 787 | 0 | |n https://doaj.org/toc/2223-330X | |
| 856 | 4 | 1 | |u https://doaj.org/article/741540d23e2b4fef8cae6edfe91f6e13 |z Connect to this object online. |