Megacystis-Microcolon-intestinal hypoperistalsis syndrome

Megacystis Microcolon Intestinal Hypoperistalsis Syndrome (MMIHS) is a rare congenital anomaly that presents with severe form of functional obstruction of the gastrointestinal tract which is usually fatal. Here, we report a full term female infant with MMIHS presented with feeding intolerance, huge...

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Bibliographic Details
Main Authors: Ahmed Elrouby (Author), Mostafa Ahmed Kotb (Author), Mostafa Abdelatty (Author), Saber Waheeb (Author)
Format: Book
Published: Elsevier, 2019-02-01T00:00:00Z.
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Summary:Megacystis Microcolon Intestinal Hypoperistalsis Syndrome (MMIHS) is a rare congenital anomaly that presents with severe form of functional obstruction of the gastrointestinal tract which is usually fatal. Here, we report a full term female infant with MMIHS presented with feeding intolerance, huge abdominal distension, bile-stained vomiting, absent bowel sounds and a large abdominal cystic mass. Exploration revealed hugely distended urinary bladder, micro colon, short bowel and malrotation of the small intestine. Ladd's procedure, ileostomy and vesicostomy were performed. Keywords: Megacystitis, Microcolon, Hypoperistalysis
Item Description:2213-5766
10.1016/j.epsc.2018.11.002