Olmsted Syndrome

Olmsted syndrome is a rare congenital, sharply circumscribed transgredient palmoplantar keratoderma. It was first described by Olmsted in 1927. The diagnosis of this rare disease depends on clinical features like symmetrical involvement of keratoderma of the palms and soles and the symmetrical hyper...

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Bibliographic Details
Main Authors: Renata Elise Tonoli (Author), Damiê De Villa (Author), Renata Hübner Frainer (Author), Luana Pizzarro Meneghello (Author), Nelson Ricachnevsky (Author), Maurício de Quadros (Author)
Format: Book
Published: Hindawi Limited, 2012-01-01T00:00:00Z.
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Summary:Olmsted syndrome is a rare congenital, sharply circumscribed transgredient palmoplantar keratoderma. It was first described by Olmsted in 1927. The diagnosis of this rare disease depends on clinical features like symmetrical involvement of keratoderma of the palms and soles and the symmetrical hyperkeratotic plaques around the body orifices. It starts in the neonatal period or in childhood. The disease has a slow but progressive and extremely disabling course. Treatment of Olmsted syndrome is often based on topical therapy with retinoic acid, corticosteroid, emollients, and keratolytics. The present paper describes a case of Olmsted syndrome and its treatment.
Item Description:2090-6463
2090-6471
10.1155/2012/927305