Swyer-James syndrome in a 7-year-old female

Swyer-James syndrome is a rare syndrome that occurs as a result of repeated bronchiolitis and pneumonitis in childhood. Most cases are asymptomatic, and subsequent diagnosis may not occur until adulthood. We present the case of a 7-year-old female with Swyer-James syndrome, which was initially diagn...

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Bibliographic Details
Main Authors: Jun Mori (Author), Daisuke Kaneda (Author), Atsushi Fujiki (Author), Kenichi Isoda (Author), Tomoya Kotani (Author), Yo Ushijima (Author)
Format: Book
Published: MDPI AG, 2016-10-01T00:00:00Z.
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Summary:Swyer-James syndrome is a rare syndrome that occurs as a result of repeated bronchiolitis and pneumonitis in childhood. Most cases are asymptomatic, and subsequent diagnosis may not occur until adulthood. We present the case of a 7-year-old female with Swyer-James syndrome, which was initially diagnosed and treated as asthma. The patient developed respiratory distress and atelectasis which were treated with biphasic cuirass ventilation. This case suggests that Swyer-James syndrome should be a concern in patients with chronic cough and wheezing, and highlights the importance of taking a careful history and appropriate radiological investigations for diagnosis. Once Swyer-James syndrome is diagnosed, prophylaxis and appropriate management of respiratory infections becomes important.
Item Description:2036-749X
2036-7503
10.4081/pr.2016.6643