Recurrent intraparenchymal brain hemorrhage in an infant with factor XIII deficiency

Factor XIII deficiency is an autosomal recessive disorder with an incidence of 1 in 1-5 million. On activation factor XIII stabilizes clot formation by cross-linking fibrin strands. Deficiency is characterized by severe bleeding due to impairment in clot formation. We describe a case of a child pres...

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Main Authors: Devdeep Mukherjee (Author), Dibyendu De (Author), Satyajit Das (Author), Gopikrishna Kurasa (Author)
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Publicado: Hygeia Press di Corridori Marinella, 2021-05-01T00:00:00Z.
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Número de Clasificación: A1234.567
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