Swyer syndrome with heterotopic adrenal cortical tissue in streak gonads: A rare case and review of literature

• Main Authors: Manu Goyal (Author), Shuchita Batra (Author), Pratibha Singh (Author), Shashank Shekhar (Author), Poonam Elhence (Author)
• Format: Book
• Published: Wolters Kluwer Medknow Publications, 2019-01-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Swyer syndrome is a 46 XY pure gonadal dysgenesis. Affected individuals are phenotypically female with external female genitalia, hypoplastic Mullerian structures, and the presence of streak gonads. Gonadectomy is indicated due to increased risk of development of malignancy in streak gonads. We here...