Two cases of progressive familial intrahepatic cholestasis type 2: Role of surgery with brief review of literature

Progressive familial intrahepatic cholestasis (PFIC) is a rare bile acid transporter defect and autosomal recessive disorder with type 2 being the most common type. Partial internal or external biliary diversion delays its progression to end-stage liver disease. Here, we discuss two cases of type 2...

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מידע ביבליוגרפי
Main Authors: Hinglaj Saha (Author), Ghosh Tapanjyoti (Author), Somak Biswas (Author), Prafulla Kumar Mishra (Author), Kalyani Saha Basu (Author), Uttara Chatterjee (Author)
פורמט: ספר
יצא לאור: Wolters Kluwer Medknow Publications, 2019-01-01T00:00:00Z.
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תיאור
סיכום:Progressive familial intrahepatic cholestasis (PFIC) is a rare bile acid transporter defect and autosomal recessive disorder with type 2 being the most common type. Partial internal or external biliary diversion delays its progression to end-stage liver disease. Here, we discuss two cases of type 2 PFIC.
תאור פריט:0971-9261
1998-3891
10.4103/jiaps.JIAPS_235_17