Two cases of progressive familial intrahepatic cholestasis type 2: Role of surgery with brief review of literature
Progressive familial intrahepatic cholestasis (PFIC) is a rare bile acid transporter defect and autosomal recessive disorder with type 2 being the most common type. Partial internal or external biliary diversion delays its progression to end-stage liver disease. Here, we discuss two cases of type 2...
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Main Authors: | , , , , , |
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פורמט: | ספר |
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Wolters Kluwer Medknow Publications,
2019-01-01T00:00:00Z.
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סיכום: | Progressive familial intrahepatic cholestasis (PFIC) is a rare bile acid transporter defect and autosomal recessive disorder with type 2 being the most common type. Partial internal or external biliary diversion delays its progression to end-stage liver disease. Here, we discuss two cases of type 2 PFIC. |
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תאור פריט: | 0971-9261 1998-3891 10.4103/jiaps.JIAPS_235_17 |