Leiomyosarcoma of the Renal Vein Mimicking a Primitive Renal Cell Carcinoma: Case Report of an Unusual Presentation

Primary leiomyosarcomas (LMS) of vascular origin are rare tumors, and more than half of the cases arise in the inferior vena cava (IVC). Primary LMS of the renal vein are extremely rare tumors with only a few cases reported in the literature. Their diagnosis is made only by pathological features. Hi...

Full description

Saved in:
Bibliographic Details
Main Authors: Amal Fekkar (Author), Hafsa Elouazzani (Author), Ahmed Jahid (Author), Kaoutar Znati (Author), Fouad Zouaidia (Author), Zakia Bernoussi (Author)
Format: Book
Published: Hindawi Limited, 2021-01-01T00:00:00Z.
Subjects:
Online Access:Connect to this object online.
Tags: Add Tag
No Tags, Be the first to tag this record!

MARC

LEADER 00000 am a22000003u 4500
001 doaj_b673c3f3efcb45beb51e5dd0816ee622
042 |a dc 
100 1 0 |a Amal Fekkar  |e author 
700 1 0 |a Hafsa Elouazzani  |e author 
700 1 0 |a Ahmed Jahid  |e author 
700 1 0 |a Kaoutar Znati  |e author 
700 1 0 |a Fouad Zouaidia  |e author 
700 1 0 |a Zakia Bernoussi  |e author 
245 0 0 |a Leiomyosarcoma of the Renal Vein Mimicking a Primitive Renal Cell Carcinoma: Case Report of an Unusual Presentation 
260 |b Hindawi Limited,   |c 2021-01-01T00:00:00Z. 
500 |a 2090-6781 
500 |a 2090-679X 
500 |a 10.1155/2021/6637533 
520 |a Primary leiomyosarcomas (LMS) of vascular origin are rare tumors, and more than half of the cases arise in the inferior vena cava (IVC). Primary LMS of the renal vein are extremely rare tumors with only a few cases reported in the literature. Their diagnosis is made only by pathological features. Histologically, they are made of atypical spindle-shaped cells arranged in long intersecting fascicles. Tumor cells stain positive for myogenic markers in immunohistochemistry. Standard treatment consists of radical nephrectomy followed by chemotherapy and/or radiotherapy. Because of insufficient histological data and follow-up, the prognosis factors are not well identified. Overall prognosis of renal vein LMS is poor. We report here an exceptional case of a huge LMS of the right renal vein mimicking a primitive renal cell carcinoma, occurring in a 56-year-old male patient. 
546 |a EN 
690 |a Pathology 
690 |a RB1-214 
655 7 |a article  |2 local 
786 0 |n Case Reports in Pathology, Vol 2021 (2021) 
787 0 |n http://dx.doi.org/10.1155/2021/6637533 
787 0 |n https://doaj.org/toc/2090-6781 
787 0 |n https://doaj.org/toc/2090-679X 
856 4 1 |u https://doaj.org/article/b673c3f3efcb45beb51e5dd0816ee622  |z Connect to this object online.