Genital Hailey- Hailey disease: a case report
Hailey - Hailey disease is a rare autosomal dominant acantholytic disorder, previously not reported from Nepal. We report a case of 30 years old female who presented with pruritic hyperkeratotic papules and plaques on vulva, perianal area and inner left thigh for a period of one year. Biopsy from th...
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| Main Authors: | , , , , |
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| Format: | Book |
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Our Dermatology Online,
2013-01-01T00:00:00Z.
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| Summary: | Hailey - Hailey disease is a rare autosomal dominant acantholytic disorder, previously not reported from Nepal. We report a case of 30 years old female who presented with pruritic hyperkeratotic papules and plaques on vulva, perianal area and inner left thigh for a period of one year. Biopsy from the lesion showed suprabasal acantholysis with loss of intercellular bridges resulting in a dilapidated brick-wall appearance; characteristic of Hailey - Hailey disease. Treatment of this disease till date is far from satisfactory. |
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| Item Description: | 2081-9390 |