A female case of pleuropulmonary blastoma type 1 whose pulmonary cystic lesion was followed since neonate
Pleuropulmonary blastoma (PPB) is a rare malignant mesenchymal tumor. It is classified into 3 subgroups, and PPB type 1 is known to be a cystic lesion with good prognosis. Here, we report a case of PPB type 1 seen in a 1-year-old girl whose pulmonary cystic lesion had been followed-up as a congenita...
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| Main Authors: | , , , , , , , , , , , , , , , , , , , |
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Elsevier,
2017-04-01T00:00:00Z.
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| 042 | |a dc | ||
| 100 | 1 | 0 | |a Michinobu Ohno |e author |
| 700 | 1 | 0 | |a Toshiko Takezoe |e author |
| 700 | 1 | 0 | |a Toshihiko Watanabe |e author |
| 700 | 1 | 0 | |a Kazunori Tahara |e author |
| 700 | 1 | 0 | |a Tomoro Hishiki |e author |
| 700 | 1 | 0 | |a Akihiro Fujino |e author |
| 700 | 1 | 0 | |a Motomi Matsuo |e author |
| 700 | 1 | 0 | |a Masataka Higuchi |e author |
| 700 | 1 | 0 | |a Kazuteru Kawasaki |e author |
| 700 | 1 | 0 | |a Yoko Shioda |e author |
| 700 | 1 | 0 | |a Motohiro Kato |e author |
| 700 | 1 | 0 | |a Chikako Kiyotani |e author |
| 700 | 1 | 0 | |a Kimikazu Matsumoto |e author |
| 700 | 1 | 0 | |a Emi Takakuwa |e author |
| 700 | 1 | 0 | |a Rie Irie |e author |
| 700 | 1 | 0 | |a Takako Yoshioka |e author |
| 700 | 1 | 0 | |a Shunsuke Kimura |e author |
| 700 | 1 | 0 | |a Masafumi Seki |e author |
| 700 | 1 | 0 | |a Junko Takita |e author |
| 700 | 1 | 0 | |a Yutaka Kanamori |e author |
| 245 | 0 | 0 | |a A female case of pleuropulmonary blastoma type 1 whose pulmonary cystic lesion was followed since neonate |
| 260 | |b Elsevier, |c 2017-04-01T00:00:00Z. | ||
| 500 | |a 2213-5766 | ||
| 500 | |a 10.1016/j.epsc.2017.02.009 | ||
| 520 | |a Pleuropulmonary blastoma (PPB) is a rare malignant mesenchymal tumor. It is classified into 3 subgroups, and PPB type 1 is known to be a cystic lesion with good prognosis. Here, we report a case of PPB type 1 seen in a 1-year-old girl whose pulmonary cystic lesion had been followed-up as a congenital pulmonary airway malformation since neonate. The cyst had been diagnosed as congenital pulmonary airway malformation before surgery but the final diagnosis was type 1 PPB. The tumor had a somatic mutation in exon 25 of the DICER 1 gene whereas no germline mutation was found. | ||
| 546 | |a EN | ||
| 690 | |a Pleuropulmonary blastoma type 1 | ||
| 690 | |a Cystic lung disease | ||
| 690 | |a CPAM | ||
| 690 | |a DICER1 | ||
| 690 | |a Pediatrics | ||
| 690 | |a RJ1-570 | ||
| 690 | |a Surgery | ||
| 690 | |a RD1-811 | ||
| 655 | 7 | |a article |2 local | |
| 786 | 0 | |n Journal of Pediatric Surgery Case Reports, Vol 19, Iss C, Pp 34-37 (2017) | |
| 787 | 0 | |n http://www.sciencedirect.com/science/article/pii/S2213576617300234 | |
| 787 | 0 | |n https://doaj.org/toc/2213-5766 | |
| 856 | 4 | 1 | |u https://doaj.org/article/bfa0e7e8512d4da4892e4872a96cd34d |z Connect to this object online. |