Pulmonary agenesis and respiratory failure in childhood

• Những tác giả chính: Paula Vanessa Valverde Dinamarco (Tác giả), Cesar Cilento Ponce (Tác giả)
• Định dạng: Sách
• Được phát hành: University of São Paulo, 2015-03-01T00:00:00Z.
• Những chủ đề: article
• Truy cập trực tuyến: Connect to this object online.
• Notes: 10.4322/acr.%y.98453; 2236-1960
• Keywords: Lung agenesis; Respiratory Insufficiency; Autopsy; Medicine; R; Internal medicine; RC31-1245
• Source: Autopsy and Case Reports, Vol 5, Iss 1 (2015)

Pulmonary agenesis (PA) is a rare congenital anomaly, which may be unilateral or bilateral. Unilateral PA may be associated with nonspecific respiratory symptoms. We report the case of 5-month-old infant who presented a normal development until the age of 4 months when a respiratory infection caused an acute respiratory distress syndrome with a fatal outcome. The autopsy findings depicted the right lung agenesis without any other concomitant malformation. Although respiratory symptoms represent frequent complaints in pediatrics, the aim of this study is not only to draw attention to the unilateral pulmonary agenesis as a possible underlying malformation in children who present recurrent and severe respiratory symptoms, but also to report a case diagnosed at autopsy.