Anesthesia in Treacher Collins Syndrome for bone anchored hearing aid (BAHA) surgery.

• Main Authors: S. Sorrenti (Author), E. Pisello (Author), M. Ciuffreda (Author), L. Brugiaferri (Author), J. Silvestri (Author), F. Lacchè (Author), G. Castellana (Author), A. Buonamico (Author), A. Pennacchi (Author), C. Piangatelli (Author), D. Galante (Author)
• Format: Book
• Published: Pediatric Anesthesia and Critical Care Journal, 2023-07-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Summary

Treacher Collins syndrome (TCS) is a rare genetic disor- der characterized by distinctive abnormalities of the head and face, affecting about one child in every 50000. Ab- normalities such micrognathia, cleft palate and cervical spine alterations are common and may represent an addi- tional risk in airway management for general anesthesia. As a matter of fact, difficult OTI prevalence in paediatric surgery rises from 1-2% to 50% when considering the subpopulation of paediatric patients with cervical spine diseases, as TCS ones. This article describes a case report of our anesthesiological management in bone-anchored hearing aid (BAHA) implant surgery in a 7-year-old fe- male Treacher Collins Syndrome patient born without the long process of the incus, the stapes and with hypoplasia of the oval window bilaterally. A careful preoperative evaluation and anesthesiological plan based on the use of videolaryngoscopy, routine practice in our centre, granted a successful outcome and no complications.

Item Description

10.14587/paccj.2023.11
2281-8421