Triple "A" syndrome presenting as recurrent chronic sinusitis with Pneumonia, septic shock and meningoencephalitis in a child

• Principais autores: Ramaning Loni (Autor), Priyanka Agrawal (Autor), Prashant Rajebhosale (Autor), Mrutyunjaya Panda (Autor), Prashant Darveshi (Autor), Prakash Valse (Autor)
• Formato: Livro
• Publicado em: Wolters Kluwer Medknow Publications, 2018-01-01T00:00:00Z.
• Assuntos: article
• Acesso em linha: Connect to this object online.

Triple A syndrome (All grove syndrome) is a rare autosomal recessive disorder characterized by the clinical triads of adrenal insufficiency, achalasia cardia and alacrimia with variable association of autonomic and neurological manifestations. Nearly100 cases have been reported all over world howeve...