Dorsal teratoma simulating an upper limb associated with a diastematomyelia

• Main Authors: Ahmed Kane (Author), Ahmed Salem Kleib (Author), Cheikh Diouf (Author), Sidi Mohamed Nagi (Author), Elhadj Ada (Author), Yacoub Mohamed Sghair (Author), Sidi Wafi Baba (Author)
• Format: Book
• Published: Elsevier, 2021-01-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.
• Notes: 2213-5766; 10.1016/j.epsc.2020.101715
• Keywords: Diastomatomyelia; Teratoma; Neutomelia; Pediatrics; RJ1-570; Surgery; RD1-811
• Source: Journal of Pediatric Surgery Case Reports, Vol 64, Iss , Pp 101715- (2021)

Introduction: The association of a diastematomyelia with a dorsal teratoma simulating an accessory limb is a very rare condition, the management of which being controversial. Observation: A female newborn presented to us for the management of a dorsal midline mass simulating an upper extremity. The rest of the clinical exam and particularly the neurologic exam were normal. A complete CT scan and a thoracic and lumbar MRI confirmed a diastematomyelia type I and a structure appearing as an incomplete upper extremity possessing a scapula, a humerus, and two digits arising from a widening between the vertebral column. The surgical resections of this apparent accessory limb were accomplished without complications. The pathologic examination showed a mature teratoma with gastro-intestinal, cutaneous, and cartilaginous tissues. Conclusion: A newborn presenting with a dorsal mass simulating an accessory limb must have a CT-scan and an MRI to detect associated split cord malformation (SCM).