Rosai-Dorfman disease presenting with extensive cutaneous manifestation - Case report Doença de Rosai-Dorfman com manifestação cutânea extensa - Relato de caso

• Main Authors: Paula Azevedo Borges Leal (Author), Adrilena Lopes Adriano (Author), Marcelle Parente Breckenfeld (Author), Igor Santos Costa (Author), Antônio Renê Diógenes de Sousa (Author), Heitor de Sá Gonçalves (Author)
• Format: Book
• Published: Sociedade Brasileira de Dermatologia, 2013-04-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Rosai-Dorfman disease is a benign, self-limited, idiopathic proliferative histiocytic disorder. It was first described in 1969 by Rosai and Dorfman. In its typical form the disease is characterized by extensive cervical lymphadenopathy associated with fever, polyclonal gammopathy and leukocytosis wi...