Non-familial cherubism: A case report with its surgical management

Cherubism is an autosomal-dominant inherited syndrome; it starts in early childhood and involutes by puberty. It is characterized by excessive bone degradation of the jaws and development of fibrous tissue masses. Non-familial cherubism is a rare entity, which needs to be documented. This paper desc...

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Main Authors: Shital A Hungund (Author), Vatsala Singh (Author), Chaitra Nagaraja (Author)
Format: Book
Published: Wolters Kluwer Medknow Publications, 2013-01-01T00:00:00Z.
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100 1 0 |a Shital A Hungund  |e author 
700 1 0 |a Vatsala Singh  |e author 
700 1 0 |a Chaitra Nagaraja  |e author 
245 0 0 |a Non-familial cherubism: A case report with its surgical management 
260 |b Wolters Kluwer Medknow Publications,   |c 2013-01-01T00:00:00Z. 
500 |a 0972-124X 
500 |a 10.4103/0972-124X.124532 
520 |a Cherubism is an autosomal-dominant inherited syndrome; it starts in early childhood and involutes by puberty. It is characterized by excessive bone degradation of the jaws and development of fibrous tissue masses. Non-familial cherubism is a rare entity, which needs to be documented. This paper describes the findings of non-familial cherubism. An 11-year-old male patient reported with bilateral swellings of the jaws and unerupted teeth. Extensive gingival overgrowth, cherubic facial appearance, multilocular osteolytic lesions in radiographs and family history lead to the diagnosis of non-familial cherubism. Treatment included full mouth excision of the gingival tissue by gingivectomy with both manual instrumentation and electrosurgery. Patient is being monitored and recalled for frequent follow-ups. Dental practitioners need to be alert with patients presenting with gingival overgrowth. 
546 |a EN 
690 |a Cherubism 
690 |a fibromatosis gingivae 
690 |a fibro-osseous lesions 
690 |a gingivectomy 
690 |a Dentistry 
690 |a RK1-715 
655 7 |a article  |2 local 
786 0 |n Journal of Indian Society of Periodontology, Vol 17, Iss 6, Pp 816-818 (2013) 
787 0 |n http://www.jisponline.com/article.asp?issn=0972-124X;year=2013;volume=17;issue=6;spage=816;epage=818;aulast=Hungund 
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856 4 1 |u https://doaj.org/article/eb5015960182458a9cda3c56e54d79c1  |z Connect to this object online.