Peutz-Jeghers syndrome: A circumventable emergency

Peutz-Jeghers syndrome (PJS) is characterized by multiple hamartomatous polyps in the gastrointestinal tract and mucocutaneous pigmentation. Here we present, a case of multiple gastrointestinal hamartomatous polyps in a 22-year-old male who had been operated for intestinal obstruction due to ileocol...

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Main Authors: Sourav Choudhury (Author), Anupam Das (Author), Priyankar Misra (Author), Udipta Ray (Author), Sujata Sarangi (Author)
Format: Book
Published: Wolters Kluwer Medknow Publications, 2018-01-01T00:00:00Z.
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100 1 0 |a Sourav Choudhury  |e author 
700 1 0 |a Anupam Das  |e author 
700 1 0 |a Priyankar Misra  |e author 
700 1 0 |a Udipta Ray  |e author 
700 1 0 |a Sujata Sarangi  |e author 
245 0 0 |a Peutz-Jeghers syndrome: A circumventable emergency 
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520 |a Peutz-Jeghers syndrome (PJS) is characterized by multiple hamartomatous polyps in the gastrointestinal tract and mucocutaneous pigmentation. Here we present, a case of multiple gastrointestinal hamartomatous polyps in a 22-year-old male who had been operated for intestinal obstruction due to ileocolic intussusception. Resection of the affected segment was done with proximal ileostomy and distal mucous fistula formation. Clinicopathological diagnosis of PJS was made. Later, during ileostomy closure, it was found that the patient had a transverse colonic mass which was resected. Histological examination with immunohistochemistry confirmed it to be a Mucosa-Associated Lymphoid Tissue Lymphoma (MALToma). Colonic MALToma in the background of PJS is a unique case for which it has been reported. 
546 |a EN 
690 |a Colonic Mucosa-Associated Lymphoid Tissue Lymphoma 
690 |a intussusception 
690 |a Peutz-Jeghers syndrome 
690 |a Dermatology 
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655 7 |a article  |2 local 
786 0 |n Indian Journal of Dermatology, Vol 63, Iss 2, Pp 168-171 (2018) 
787 0 |n http://www.e-ijd.org/article.asp?issn=0019-5154;year=2018;volume=63;issue=2;spage=168;epage=171;aulast=Choudhury 
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