Extensive Extragenital Lichen Sclerosus-Like Lesions in a Patient with Junctional Epidermolysis Bullosa

Epidermolysis bullosa (EB) is a heterogeneous group of genetic disorders characterized by the formation of blisters either spontaneously or at the sites of trauma. These heal with post-inflammatory hypopigmentation, scarring, or milia formation. We hereby present a child who presented with widesprea...

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Bibliographic Details
Main Authors: Smriti Gupta (Author), Sanjeev Handa (Author), Debajyoti Chatterjee (Author), Dipankar De (Author), Rahul Mahajan (Author)
Format: Book
Published: Wolters Kluwer Medknow Publications, 2024-08-01T00:00:00Z.
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Summary:Epidermolysis bullosa (EB) is a heterogeneous group of genetic disorders characterized by the formation of blisters either spontaneously or at the sites of trauma. These heal with post-inflammatory hypopigmentation, scarring, or milia formation. We hereby present a child who presented with widespread hypopigmented atrophic areas, blistering at trauma-prone sites, and nail dystrophy. The significance of this particular case lies in the challenge of distinguishing between epidermolysis bullosa and bullous extragenital lichen sclerosus et atrophicus.
Item Description:2229-5178
2249-5673
10.4103/idoj.idoj_503_23