Multiple primary cutaneous plasmacytoma: first reported case in Brazil Plasmocitoma cutâneo primário múltiplo: primeiro caso relatado no Brasil

Primary cutaneous plasmacytoma is a rare disease characterized by monoclonal proliferation of plasma cells in the skin, in the absence of bone or systemic disease. It can be solitary or multiple, the latter being even more rare and presenting a higher mortality rate. We describe the clinical, histop...

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Bibliographic Details
Main Authors: Thais Lima Saback (Author), Luciane Francisca Fernandes Botelho (Author), Milvia Maria Simões da Silva Enokihara (Author), Nilceo Schwery Michalany (Author), Marcos César Floriano (Author)
Format: Book
Published: Sociedade Brasileira de Dermatologia, 2012-08-01T00:00:00Z.
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Summary:Primary cutaneous plasmacytoma is a rare disease characterized by monoclonal proliferation of plasma cells in the skin, in the absence of bone or systemic disease. It can be solitary or multiple, the latter being even more rare and presenting a higher mortality rate. We describe the clinical, histopathological and immunohistochemical aspects as well as the evolution of an 87-year-old female patient, diagnosed as having multiple primary cutaneous plasmacytomas.<br>O plasmocitoma cutâneo primário é uma entidade rara, caracterizada pela proliferação monoclonal de plasmócitos na pele, na ausência de doença óssea ou sistêmica. Pode ser único ou múltiplo, sendo esta última forma ainda mais rara e de pior prognóstico. Descreveremos os aspectos clínicos, histopatológicos, imunohistoquímicos e a evolução de um caso de paciente do sexo feminino, 87 anos, com diagnóstico de plasmocitoma cutâneo primário com múltiplas lesões.
Item Description:10.1590/S0365-05962012000400020
0365-0596
1806-4841