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Case report: Experience of a rare case of rebound of the Kasabach-Merritt phenomenon during sirolimus treatment in kaposiform hemangioendothelioma

Kaposiform hemangioendothelioma (KHE) is a rare vascular neoplasm associated with the Kasabach-Merritt phenomenon (KMP), which is a consumptive coagulopathy with associated potentially life-threatening thrombocytopenia. There are no standardized treatment protocols for the management of KHE with KMP...

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Bibliographic Details
Main Authors: Liang Wang (Author), Jing Li (Author), Changhua Wu (Author), Dan Song (Author), Zhuang Liu (Author), Yanli Niu (Author), Jie Zhou (Author), Lei Guo (Author)
Format: Book
Published: Frontiers Media S.A., 2022-08-01T00:00:00Z.
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Summary:Kaposiform hemangioendothelioma (KHE) is a rare vascular neoplasm associated with the Kasabach-Merritt phenomenon (KMP), which is a consumptive coagulopathy with associated potentially life-threatening thrombocytopenia. There are no standardized treatment protocols for the management of KHE with KMP. Moreover, there are limited reports regarding the treatment of cases of rebound. Herein, we describe a rare case of rebound of KHE/KMP, during systemic sirolimus treatment, successfully treated with embolization and vincristine infusion combined with microwave ablation.
Item Description:2296-2360
10.3389/fped.2022.949950

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