Squamous-cell carcinoma in a female patient suffering from recessive dystrophic epidermolysis bullosa

The article describes a case of squamous-cell carcinoma in a female patient aged 30 suffering from a rare inherited disease -recessive dystrophic epidermolysis bullosa (RDEB). RDEB is characterized by a high risk of squamous cell carcinoma in young patients. The most frequent form is a highly differ...

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Main Authors: A. E. Karamova (Author), V. V. Chikin (Author), V. I. Albanova (Author), V. A. Smolyannikova (Author), M. A. Nefedova (Author), E. S. Monchakovskaya (Author)
Format: Book
Published: State Scientific Center of Dermatovenereology and Cosmetology, 2017-08-01T00:00:00Z.
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042 |a dc 
100 1 0 |a A. E. Karamova  |e author 
700 1 0 |a V. V. Chikin  |e author 
700 1 0 |a V. I. Albanova  |e author 
700 1 0 |a V. A. Smolyannikova  |e author 
700 1 0 |a M. A. Nefedova  |e author 
700 1 0 |a E. S. Monchakovskaya  |e author 
245 0 0 |a Squamous-cell carcinoma in a female patient suffering from recessive dystrophic epidermolysis bullosa 
260 |b State Scientific Center of Dermatovenereology and Cosmetology,   |c 2017-08-01T00:00:00Z. 
500 |a 0042-4609 
500 |a 2313-6294 
500 |a 10.25208/0042-4609-2016-0-3-83-89 
520 |a The article describes a case of squamous-cell carcinoma in a female patient aged 30 suffering from a rare inherited disease -recessive dystrophic epidermolysis bullosa (RDEB). RDEB is characterized by a high risk of squamous cell carcinoma in young patients. The most frequent form is a highly differentiated form of cancer characterized by an aggressive course with the early development of metastases and fast progression, which is the most frequent cause of death in RDEB patients. The described case of squamous cell carcinoma in a young female RDEB patient emphasizes the role of early tumor diagnostics. 
546 |a EN 
546 |a RU 
690 |a врожденный буллезный эпидермолиз 
690 |a рецессивный дистрофический буллезный эпидермолиз 
690 |a плоскоклеточный рак кожи 
690 |a hereditary epidermolysis bullosa 
690 |a recessive dystrophic epidermolysis bullosa 
690 |a squamous-cell carcinoma 
690 |a Dermatology 
690 |a RL1-803 
655 7 |a article  |2 local 
786 0 |n Vestnik Dermatologii i Venerologii, Vol 0, Iss 3, Pp 83-89 (2017) 
787 0 |n https://www.vestnikdv.ru/jour/article/view/243 
787 0 |n https://doaj.org/toc/0042-4609 
787 0 |n https://doaj.org/toc/2313-6294 
856 4 1 |u https://doaj.org/article/fd2ef1efb0dd47a7a9d5ce891f244e6c  |z Connect to this object online.