Severe polycystic liver disease: An unsual cause of chronic Budd-Chiari Syndrome
<p>Autosomal dominant polycystic kidney disease is a hereditary disease, characterized by the development of cysts in the renal parenchyma with extra-renal manifestations. Liver damage is rarely a source of complications. A Budd-Chiari syndrome could occur following the compression of the supr...
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Archives of Clinical Gastroenterology - Peertechz Publications,
2022-10-29.
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LEADER | 00000 am a22000003u 4500 | ||
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001 | peertech__10_17352_2455-2283_000113 | ||
042 | |a dc | ||
100 | 1 | 0 | |a Aboutarik Fatima Ezzahra |e author |
700 | 1 | 0 | |a Dassouli Cherihane |e author |
700 | 1 | 0 | |a Ait Errami Adil |e author |
700 | 1 | 0 | |a Oubaha Sofia |e author |
700 | 1 | 0 | |a Samlani Zouhour |e author |
700 | 1 | 0 | |a Krati Khadija |e author |
245 | 0 | 0 | |a Severe polycystic liver disease: An unsual cause of chronic Budd-Chiari Syndrome |
260 | |b Archives of Clinical Gastroenterology - Peertechz Publications, |c 2022-10-29. | ||
520 | |a <p>Autosomal dominant polycystic kidney disease is a hereditary disease, characterized by the development of cysts in the renal parenchyma with extra-renal manifestations. Liver damage is rarely a source of complications. A Budd-Chiari syndrome could occur following the compression of the supra-hepatic veins by the cysts. It is an exceptional mechanical complication. </p><p>We present a case of a 54 year old woman, with a diagnostic of an asymptomatic autosomal dominat polycystic kidney disease since childhood was admitted to our hospital due to significantly increased abdominal girth. The physical examination showed grade III ascites. A paracentesis for relief at admission disclosed an exudative fluid. A abdominal computed tomographic scan showed multiples cystic lesions in the kidneys and liver, with a large hepatic cyst responsible for compression of the suprahepatic veins and the inferior vena cava resulting in chronic Budd-Chiari syndrome. The treatment was radiological drainage followed by percutaneous sclerosis of cysts to alleviation of the compression. Unfortunately, the patient died a few days after an intraperitoneal cystic rupture. </p> | ||
540 | |a Copyright © Aboutarik Fatima Ezzahra et al. | ||
546 | |a en | ||
655 | 7 | |a Case Report |2 local | |
856 | 4 | 1 | |u https://doi.org/10.17352/2455-2283.000113 |z Connect to this object online. |