Severe polycystic liver disease: An unsual cause of chronic Budd-Chiari Syndrome

<p>Autosomal dominant polycystic kidney disease is a hereditary disease, characterized by the development of cysts in the renal parenchyma with extra-renal manifestations. Liver damage is rarely a source of complications. A Budd-Chiari syndrome could occur following the compression of the supr...

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Main Authors: Aboutarik Fatima Ezzahra (Author), Dassouli Cherihane (Author), Ait Errami Adil (Author), Oubaha Sofia (Author), Samlani Zouhour (Author), Krati Khadija (Author)
Format: Book
Published: Archives of Clinical Gastroenterology - Peertechz Publications, 2022-10-29.
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042 |a dc 
100 1 0 |a Aboutarik Fatima Ezzahra  |e author 
700 1 0 |a  Dassouli Cherihane  |e author 
700 1 0 |a  Ait Errami Adil  |e author 
700 1 0 |a  Oubaha Sofia  |e author 
700 1 0 |a  Samlani Zouhour  |e author 
700 1 0 |a Krati Khadija  |e author 
245 0 0 |a Severe polycystic liver disease: An unsual cause of chronic Budd-Chiari Syndrome 
260 |b Archives of Clinical Gastroenterology - Peertechz Publications,   |c 2022-10-29. 
520 |a <p>Autosomal dominant polycystic kidney disease is a hereditary disease, characterized by the development of cysts in the renal parenchyma with extra-renal manifestations. Liver damage is rarely a source of complications. A Budd-Chiari syndrome could occur following the compression of the supra-hepatic veins by the cysts. It is an exceptional mechanical complication. </p><p>We present a case of a 54 year old woman, with a diagnostic of an asymptomatic autosomal dominat polycystic kidney disease since childhood was admitted to our hospital due to significantly increased abdominal girth. The physical examination showed grade III ascites. A paracentesis for relief at admission disclosed an exudative fluid. A abdominal computed tomographic scan showed multiples cystic lesions in the kidneys and liver, with a large hepatic cyst responsible for compression of the suprahepatic veins and the inferior vena cava resulting in chronic Budd-Chiari syndrome. The treatment was radiological drainage followed by percutaneous sclerosis of cysts to alleviation of the compression. Unfortunately, the patient died a few days after an intraperitoneal cystic rupture. </p> 
540 |a Copyright © Aboutarik Fatima Ezzahra et al. 
546 |a en 
655 7 |a Case Report  |2 local 
856 4 1 |u https://doi.org/10.17352/2455-2283.000113  |z Connect to this object online.