A Case Report of a Malignant Triton Tumor of the Left Retroperitoneum in a Young Female Without Neurofi bromatosis
<p>Malignant peripheral nerve sheath tumors (MPNST) are malignant cancers with origins found within peripheral nerves of various body regions-most commonly involving the buttocks, thighs, brachial plexus and para-spinal region [1]. While MPNSTs account for only 5%-10% of all soft tissue sarcom...
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Global Journal of Rare Diseases - Peertechz Publications,
2019-09-20.
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| LEADER | 00000 am a22000003u 4500 | ||
|---|---|---|---|
| 001 | peertech__10_17352_2640-7876_000016 | ||
| 042 | |a dc | ||
| 100 | 1 | 0 | |a Dayton Grogan BS |e author |
| 700 | 1 | 0 | |a Vamsi Reddy BS |e author |
| 700 | 1 | 0 | |a Earl Dane Jones |e author |
| 700 | 1 | 0 | |a Cargill H Alleyne |e author |
| 245 | 0 | 0 | |a A Case Report of a Malignant Triton Tumor of the Left Retroperitoneum in a Young Female Without Neurofi bromatosis |
| 260 | |b Global Journal of Rare Diseases - Peertechz Publications, |c 2019-09-20. | ||
| 520 | |a <p>Malignant peripheral nerve sheath tumors (MPNST) are malignant cancers with origins found within peripheral nerves of various body regions-most commonly involving the buttocks, thighs, brachial plexus and para-spinal region [1]. While MPNSTs account for only 5%-10% of all soft tissue sarcomas, there exist MPNST variations that occur with greater rarity [2]. Specifi cally, Malignant Triton Tumors (MTT) are a subset of MPNST with rhabdomyoblastic differentiation and account for only 5% of all MPNST cases [3]. MTTs were fi rst described by Mason in 1932 and found to occur in patients with Neurofi bromatosis type 1 (NF-1) in slightly more than 50% of cases. This is because sMTTs are believed to originate from Schwann cells of peripheral nerves or within existing neurofi bromas [3,4]. Diagnosis of MTT is confi rmed by immunohistochemical screening for desmin, vimentin, actin, myoglobulin, and S-100 protein.</p> | ||
| 540 | |a Copyright © Dayton Grogan BS et al. | ||
| 546 | |a en | ||
| 655 | 7 | |a Case Report |2 local | |
| 856 | 4 | 1 | |u https://doi.org/10.17352/2640-7876.000016 |z Connect to this object online. |