Spontaneous Haemomediastinum and Fatal Haemoperitoneum in woman with Vascular Ehlers-Danlos Syndrome
<p><strong>Abstract:</strong> Vascular Ehlers-Danlos Syndrome (EDS) presents with fragility of blood vessels, with high incidence of fatal hemorrhages in middle-age adults. We present a 38-year old female with vascular EDS presented to the emergency unit with spontaneous hemo...
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| Main Authors: | , , , |
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| Format: | Book |
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Archives of Pulmonology and Respiratory Care - Peertechz Publications,
2017-05-29.
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| Online Access: | Connect to this object online. |
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| Summary: | <p><strong>Abstract:</strong> Vascular Ehlers-Danlos Syndrome (EDS) presents with fragility of blood vessels, with high incidence of fatal hemorrhages in middle-age adults. We present a 38-year old female with vascular EDS presented to the emergency unit with spontaneous hemomediastinum and hemothorax. A selective arteriography showed a bronchial artery aneurysm that could be embolized. Coagulated hemothorax was cleared up using intrapleural instillation of urokinase. Acute massive hemoperitoneum happened a few hours later, due to spontaneous disruption of a splenic artery aneurysm. It could not be managed and led to the decease of the patient. Multifocal bleeding is a frequent threatening event in vascular EDS.</p> |
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| DOI: | 10.17352/aprc.000024 |