Spontaneous Haemomediastinum and Fatal Haemoperitoneum in woman with Vascular Ehlers-Danlos Syndrome
<p><strong>Abstract:</strong> Vascular Ehlers-Danlos Syndrome (EDS) presents with fragility of blood vessels, with high incidence of fatal hemorrhages in middle-age adults. We present a 38-year old female with vascular EDS presented to the emergency unit with spontaneous hemo...
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Archives of Pulmonology and Respiratory Care - Peertechz Publications,
2017-05-29.
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| LEADER | 00000 am a22000003u 4500 | ||
|---|---|---|---|
| 001 | peertech__10_17352_aprc_000024 | ||
| 042 | |a dc | ||
| 100 | 1 | 0 | |a Isabel Cal |e author |
| 700 | 1 | 0 | |a Elena Fernández |e author |
| 700 | 1 | 0 | |a Jose V Méndez |e author |
| 700 | 1 | 0 | |a Jose R Jarabo |e author |
| 245 | 0 | 0 | |a Spontaneous Haemomediastinum and Fatal Haemoperitoneum in woman with Vascular Ehlers-Danlos Syndrome |
| 260 | |b Archives of Pulmonology and Respiratory Care - Peertechz Publications, |c 2017-05-29. | ||
| 520 | |a <p><strong>Abstract:</strong> Vascular Ehlers-Danlos Syndrome (EDS) presents with fragility of blood vessels, with high incidence of fatal hemorrhages in middle-age adults. We present a 38-year old female with vascular EDS presented to the emergency unit with spontaneous hemomediastinum and hemothorax. A selective arteriography showed a bronchial artery aneurysm that could be embolized. Coagulated hemothorax was cleared up using intrapleural instillation of urokinase. Acute massive hemoperitoneum happened a few hours later, due to spontaneous disruption of a splenic artery aneurysm. It could not be managed and led to the decease of the patient. Multifocal bleeding is a frequent threatening event in vascular EDS.</p> | ||
| 540 | |a Copyright © Isabel Cal et al. | ||
| 546 | |a en | ||
| 655 | 7 | |a Case Report |2 local | |
| 856 | 4 | 1 | |u https://doi.org/10.17352/aprc.000024 |z Connect to this object online. |