Laryngeal Primary Amyloidosis: Differential Diagnosis of Localized Granulomatosis with Polyangiitis. Report of Two Cases

Laryngeal Primary Amyloidosis: Differential Diagnosis of Localized Granulomatosis with Polyangiitis. Report of Two Cases

<p>Primary laryngeal amyloidosis (PLA) and granulomatosis with polyangiitis (GPA) can present rarely with the isolated symptom of dyspnea and/or dysphonia, affecting exclusively the larynx. <br></p><p>Granulomatosis with polyangiitis is one of the anti-neutrophil cytoplasmati...

Full description

Saved in:
Bibliographic Details
Main Authors: Clarissa de Queiroz Pimentel (Author), Luciana Depiere Lanzarin (Author), Frederico Adão de Oliveira Santana (Author), Rosa Maria Rodrigues Pereira (Author), Maurício Levy-Neto (Author), Samuel Katsuyuki Shinjo (Author)
Format: Book
Published: Rheumatica Acta: Open Access - Peertechz Publications, 2017-03-08.
Subjects:
Case Report
Online Access:Connect to this object online.
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:<p>Primary laryngeal amyloidosis (PLA) and granulomatosis with polyangiitis (GPA) can present rarely with the isolated symptom of dyspnea and/or dysphonia, affecting exclusively the larynx. <br></p><p>Granulomatosis with polyangiitis is one of the anti-neutrophil cytoplasmatic antibodies (ANCA) associated vasculitis. It may be limited to the airways including may be exclusively laryngeal. This localized form of GPA has a diffi cult diagnosis because the biopsy rarely does the diagnosis and the ANCA tests are frequently negative.</p><p> In the aim of emphasizing the importance of this rare entity as a differential diag <br></p>
DOI:10.17352/raoa.000004

Similar Items