A case of dyskeratosis congenita with primary amenorrhea and adenocarcinoma of stomach

• Main Authors: Nandini Chakrabarti (Author), Nilendu Sarma (Author), Chandan Chattopadhyay (Author), Atanu Roy Chowdhuri (Author), Chanchal Das (Author), Salil K Pal (Author)
• Format: Book
• Published: Wolters Kluwer Medknow Publications, 2011-01-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Dyskeratosis congenita (DC) is a rare disease characterized by hyperpigmentation, nail dystrophy and mucous membrane abnormality. Commonly occurring in males, the patients die young usually due to bone marrow suppression. Malignancies of various descriptions have been reported in this disease, the c...