Congenital Hepatic Fibrosis in a 2-Year-Old Child Presenting with Fever of Unknown Origin

• Auteurs principaux: Michael P. Penfold (Auteur), Wentiirim B. Annankra (Auteur), Nathan C. Hull (Auteur), Margarita Corredor (Auteur)
• Format: Livre
• Publié: Hindawi Limited, 2023-01-01T00:00:00Z.
• Sujets: article
• Accès en ligne: Connect to this object online.

Congenital hepatic fibrosis is a rare, autosomal recessive, fibro-polycystic disease resulting from ductal plate malformation, leading to proliferation and fibrosis of bile ducts. Progressive hepatic fibrosis leads to portal hypertension and varices which can present with life threatening gastrointe...