Acute Pancreatitis with Rapid Clinical Improvement in a Child with Isovaleric Acidemia

Isovaleric acidemia is a rare branched-chain organic acidemia. The authors describe a 3.5-year-old girl with isovaleric acidemia and acute abdominal pain associated with bilious emesis. Elevated serum amylase and abdominal ultrasonography demonstrating an enlarged and edematous pancreas, along with...

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Main Authors: Elpis Mantadakis (Author), Ioannis Chrysafis (Author), Emmanouela Tsouvala (Author), Athanassios Evangeliou (Author), Athanassios Chatzimichael (Author)
Format: Book
Published: Hindawi Limited, 2013-01-01T00:00:00Z.
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3rd Floor Main Library

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Call Number: A1234.567
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