Early Infantile Hemophagocytic Lymphohistiocytosis Masquerading as Late-onset Sepsis: A Case Report with Review of the Literature

• Main Authors: L. Ramitha (Author), Amith Ahmed (Author), Laxmi Kamath (Author), Deepa Mohan Sharma (Author), Prathap Chandra (Author)
• Format: Book
• Published: Wolters Kluwer Medknow Publications, 2024-08-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Background: Hemophagocytic lymphohistiocytosis (HLH) is a condition due to uncontrolled overactivation of macrophages, cytotoxic T cells, and natural killer cells creating a cytokine storm, characterized by multiorgan involvement. Familial HLH (fHLH) is due to genetic defects and presents early in l...