Outcome of two pairs of monozygotic twins with pleuropulmonary blastoma: case report

• Main Authors: Shihan Zhang (Author), Xisi Wang (Author), Sihui Li (Author), Siyu Cai (Author), Tong Yu (Author), Libing Fu (Author), Na Zhang (Author), Xiaoxia Peng (Author), Qi Zeng (Author), Xiaoli Ma (Author)
• Format: Book
• Published: BMC, 2020-10-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Abstract Background Pleuropulmonary blastomas (PPB) are rare aggressive paediatric lung malignancies and are among the most common DICER1-related disorders: it is estimated that 75-80% of children with a PPB have the DICER1 mutation. DICER1 mutations are responsible for familial tumour susceptibilit...