Improvement of Erdheim-Chester disease-related renal failure after treatment with anakinra

• Main Authors: Manuel Alfredo Podestà (Author), Giorgio Graziani (Author), Francesco Reggiani (Author), Michele Buemi (Author), Salvatore Badalamenti (Author), Claudio Ponticelli (Author)
• Format: Book
• Published: The Korean Society of Nephrology, 2014-09-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis characterized by infiltrates of lipid-laden CD68+/CD1a− histiocytes, affecting heart, lungs, central nervous system, and bones. Kidney and adjacent structures can also be affected, leading to renal failure in about 30% of case...