Congenital Pulmonary Alveolar Proteinosis

• Main Authors: Saber Hammami (Author), Khaled Harrathi (Author), Khaled Lajmi (Author), Samir Hadded (Author), Chebil Ben Meriem (Author), Mohamed Néji Guédiche (Author)
• Format: Book
• Published: Hindawi Limited, 2013-01-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Pulmonary alveolar proteinosis (PAP) is a rare syndrome characterized by pulmonary surfactant accumulation within the alveolar spaces. It occurs with a reported prevalence of 0.1 per 100,000 individuals. Two clinically different pediatric types have been defined as congenital PAP which is fatal and...