Delayed appearance of mature ganglia in an infant with an atypical presentation of total colonic and small bowel aganglionosis: a case report

• Main Authors: Fereshteh Salimi Jazi (Author), Julia M. Chandler (Author), Chad M. Thorson (Author), Tiffany J. Sinclair (Author), Florette K. Hazard (Author), John A. Kerner (Author), Sanjeev Dutta (Author), James C.Y. Dunn (Author), Stephanie D. Chao (Author)
• Format: Book
• Published: BMC, 2019-04-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Abstract Background Total colonic and small bowel aganglionosis (TCSA) occurs in less than 1% of all Hirschsprung's disease patients. Currently, the mainstay of treatment is surgery. However, in patients with TCSA, functional outcomes are often poor. A characteristic transition zone in TCSA can...