Case report: A simple and reliable approach for progressive internal distraction of the sternum for Jeune syndrome (asphyxiating thoracic dystrophy): preliminary experience and literature review of surgical techniques

• Main Authors: Alessandro Inserra (Author), Angelo Zarfati (Author), Valerio Pardi (Author), Arianna Bertocchini (Author), Antonella Accinni (Author), Ivan Pietro Aloi (Author), Cristina Martucci (Author), Simone Frediani (Author)
• Format: Book
• Published: Frontiers Media S.A., 2023-09-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

BackgroundDescribed for the first time in 1954, Jeune syndrome (JS), often called asphyxiating thoracic dystrophy, is a congenital musculoskeletal disease characterized by short ribs, a narrow thorax, and small limbs. In this study, we analyzed and presented our preliminary experience with a device...