Early and sustained improvements of lung clearance index from two to sixteen weeks of elexacaftor/tezacaftor/ivacaftor therapy in patients with cystic fibrosis-a real world study

• Главные авторы: Dorothea Appelt (Автор), Gratiana Steinkamp (Автор), Sarah Sieber (Автор), Helmut Ellemunter (Автор)
• Формат: ‌
• Опубликовано: Frontiers Media S.A., 2023-03-01T00:00:00Z.
• Предметы: article
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Since the introduction of CFTR modulator therapies, longitudinal real-life data of lung clearance index (LCI) during treatment is scarce. In this single-centre, post-approval setting, we report data of 51 patients with different stages of lung disease, age 2-52 years with repeated measurements of fo...