Síndrome de Prune Belly com fístula vesicocutânea: relato de caso raro e revisão da literatura

• Main Authors: Debora Leticia Silva Gouvêa Viana (Author), Naara Rafaela Gonçalves (Author), Álvaro Henrique Anghietti Nalon (Author), Michel Correia Viana (Author), Rúbia Cecília Barbone e Melo (Author), Ítalo Guilherme Giarola de Freitas Mariano (Author), Raquel Ida Ferreira (Author), Thais Silva Maia (Author), Paula Silva Maia (Author)
• Format: Book
• Published: Sociedade Brasileira de Pediatria, 2023-12-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Prune Belly syndrome (PBS) is a rare complex malformation that preferentially affects male newborns. It presents with a wide spectrum of alterations that include abdominal muscle deficiency, varying degrees of renal dysplasia and urinary tract obstruction, in addition to bilateral cryptorchidism. In...