Incontinentia pigmenti

• Main Authors: Claudia Schermann Poziomczyk (Author), Julia Kanaan Recuero (Author), Luana Bringhenti (Author), Fernanda Diffini Santa Maria (Author), Carolina Wiltgen Campos (Author), Giovanni Marcos Travi (Author), Andre Moraes Freitas (Author), Marcia Angelica Peter Maahs (Author), Paulo Ricardo Gazzola Zen (Author), Marilu Fiegenbaum (Author), Sheila Tamanini de Almeida (Author), Renan Rangel Bonamigo (Author), Ana Elisa Kiszewski Bau (Author)
• Format: Book
• Published: Sociedade Brasileira de Dermatologia, 2014-01-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Incontinentia pigmenti is a rare genodermatosis in which the skin involvement occurs in all patients. Additionally, other ectodermal tissues may be affected, such as the central nervous system, eyes, hair, nails and teeth. The disease has a X-linked dominant inheritance pattern and is usually lethal...