Presentation of Congenital Portosystemic Shunts in Children

• Main Authors: Atessa Bahadori (Author), Beatrice Kuhlmann (Author), Dominique Debray (Author), Stephanie Franchi-Abella (Author), Julie Wacker (Author), Maurice Beghetti (Author), Barbara E. Wildhaber (Author), Valérie Anne McLin (Author), on behalf of the IRCPSS (Author)
• Format: Book
• Published: MDPI AG, 2022-02-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Background: Congenital portosystemic shunts (CPSS) are rare vascular anomalies resulting in communications between the portal venous system and the systemic venous circulation, affecting an estimated 30,000 to 50,000 live births. CPSS can present at any age as a multi-system disease of variable seve...