Proteus Syndrome: Report of Intra-Abdominal Lipomatosis

• Main Authors: Basak Erginel (Author), Melih Akin (Author), Abdullah Yildiz (Author), Cetin Karadag (Author), Nihat Sever (Author), Canan Tanik (Author), Mehmet Erturk (Author), Ali Ihsan Dokucu (Author)
• Format: Book
• Published: Georg Thieme Verlag KG, 2013-04-01T00:00:00Z.
• Subjects: article
• Online Access: Connect to this object online.

Abstract Proteus syndrome (PS) is an extremely rare sporadic disorder that manifests as an asymmetric, disproportionate overgrowth of any connective tissues, such as bone, fat, or epidermal nevi, in a mosaic or patchy pattern. This hamartoneoplastic syndrome was first described by Cohen and Hayden....